Botryoid rhabdomyosarcoma of the urogenital sinus. Apropos of 1 case in an 11 month old child
Rarivomanana, M.; Vololonantenaina, C.R.; Valikara, S.; Rakotomanga, P.; Randrianasolo, O.; Chouteau, Y.
Bulletin de la Societe de Pathologie Exotique 93(1): 29-30
2000
ISSN/ISBN: 0037-9085 PMID: 10774491 Document Number: 516411
Rhabdomyosarcomas are the most common sarcomas of the soft tissues found in children under 15 years. The reported observation is of a vaginal tumour having developed in an eleven-month-year-old little girl. It was a typical botryoid rhabdomyosarcoma, usually found in the hollow organs surrounded on the edges by mucus. Rhabdomyosarcomas have many characteristics which vary greatly according to the degree of their cellular differenciation. The majority of these tumours can be classified into four histological categories: embryonic, botryoid, alveolar or plemorphous. The treatment is exeresis surgery with radio- and chemotherapy. Prognosis, however, remains dim despite the therapeutic advances of the last few years.