Incontinentia pigmenti (Bloch-Sulzberger syndrome) : report of case
Welbury, T.A.; Welbury, R.R.
Asdc Journal of Dentistry for Children 66(3): 213-5 155
1999
ISSN/ISBN: 1945-1954 PMID: 10476362 Document Number: 503144
Incontinentia Pigmenti is an inherited disorder with predominantly ectodermal abnormalities. The dental effects, delayed eruption, hypodontia, and microdontia, are very similar to anhidrotic ectodermal dysplasia. It is important that children with incontinentia pigmenti gain access to specialist dental care including pediatric dentistry, orthodontics, prosthodontics and oral surgery.