Incontinentia pigmenti and Behçet's syndrome: an unusual combination
Menni, S.; Piccinno, R.; Biolchini, A.; Delle Piane, R.M.; Bardare, M.
Acta Dermato-Venereologica 66(4): 351-354
1986
ISSN/ISBN: 0001-5555 PMID: 2430411 Document Number: 281394
We describe an unusual case of a child who had had incontinentia pigmenti from birth and developed the clinical picture of Behçet's syndrome at five years of age. Among the various investigations performed, chemotactic activity of the polymorphonuclear leukocyte was found to be low. We discuss the possibility that there are common immunological abnormalities in the two syndromes.