Multiple trichodiscomas associated with colonic polyposis
Le Guyadec, T.; Dufau, J.P.; Poulain, J.F.; Vaylet, F.; Grossin, M.; Lanternier, G.
Annales de Dermatologie et de Venereologie 125(10): 717-719
1998
ISSN/ISBN: 0151-9638 PMID: 9835964 Document Number: 488913
Trichodiscoma is an uncommon benign tumor of the pilosebaceous system. An 83-year-old man had a past history of adenomatous polyps of the colon. The subject's brother had died from cancer of the colon. Over the past 4 years, the patient had developed approximately 30 small asymptomatic papulonodular tumors on the trunk. Skin biopsy demonstrated trichodiscomas. Together with fibrofolliculomas and perifollicular fibromas, trichodiscomas are benign tumors of the pilosebaceous system. These different tumors may occur simultaneously as in Birt-Hogg-Dubé syndrome which associates trichodiscoma and familial colonic polyposis. This combination has only been reported in Birt-Hogg-Dubé syndrome or with perifollicular fibromas. This case suggests that patients with hamartomas of the pilosebaceous system should undergo explorations in search for digestive tract polyposis.