Pseudomyxoma peritonei
Dejong, C.H.; Booster, M.H.; Theunissen, P.H.; Beets, G.L.; van Duin, C.J.
Nederlands Tijdschrift Voor Geneeskunde 141(24): 1196-1198
1997
ISSN/ISBN: 0028-2162 PMID: 9380155 Document Number: 483255
Pseudomyxoma peritonei was diagnosed in 3 men aged 38, 66 and 54 years with weight loss and distension of the abdomen. Pseudomyxoma peritonei results from seeding of the peritoneal cavity with mucus-producing epithelium. The disease is traditionally characterized by accumulation of huge amounts of mucinous ascites, relatively long survival and absence of distant, extraperitoneal metastases. Mostly, the primary tumour is an appendicular adenoma or adenocarcinoma. Sometimes, the primary tumor is localized in the ovaries. Extensive surgical debulking with postoperative intraperitoneal chemotherapy appears to be the treatment of choice.