Clear cell sarcoma of the kidney relapsing after 10 years of asymptomatic evolution
Charafe, E.; Penault-Llorca, F.; Mathoulin-Portier, M.P.; Bladou, F.; Delpéro, J.R.; Prime-Guitton, C.; Vieillefond, A.; Xerri, L.; Hassoun, J.
Annales de pathologie 17(6): 400-402
1997
ISSN/ISBN: 0242-6498 PMID: 9526627 Document Number: 482161
We report the case of a kidney tumor occurring in a thirteen year-old girl. This tumor was first diagnosed and treated as a benign one. After ten years without recurrence, a relapse occurred. The diagnosis was recurrent clear cell sarcoma of the kidney. The course in our case is uncommon because clear cell sarcoma of the kidney is a rare and aggressive pediatric neoplasm, usually characterized by a predilection for bone metastases, and a mid survival rate of 30 months without treatment.