C5 deficiency in a patient with primary Sjögren's syndrome
Schoonbrood, T.H.; Hannema, A.; Fijen, C.A.; Markusse, H.M.; Swaak, A.J.
Journal of Rheumatology 22(7): 1389-1390
1995
ISSN/ISBN: 0315-162X PMID: 7562780 Document Number: 439269
We report a case of C5 deficiency in combination with Sjogren's syndrome (SS). Our patient presented with polyarthritis and complaints of oral and ocular dryness. In the serum there was a very low titer of total hemolytic complement (CH50) due to a deficiency of the fifth complement component. C5 deficiency is often associated with recurrent life threatening infections, membranous glomerulonephritis, and discoid lupus erythematosus, but it has not been described in association with primary SS.
Document emailed within 1 workday
Related Documents
Varga, M.; Kiss, A. 1991: Malignant B-cell lymphoma in a patient with primary Sjögren syndrome Orvosi Hetilap 132(1): 29-32Papadopoulos, V.; Micheli, A.; Nikiforidis, D.; Mimidis, K. 2005: Primary biliary cirrhosis complicated by transverse myelitis in a patient without Sjögren's syndrome Journal of Postgraduate Medicine 51(1): 43-44
Stroehmann, A.; Dörner, T.; Lukowsky, A.; Feist, E.; Hiepe, F.; Burmester, G-Rüdiger. 2002: Cutaneous T cell lymphoma in a patient with primary biliary cirrhosis and secondary Sjögren's syndrome Journal of Rheumatology 29(6): 1326-1329
Brito-Zerón, P.; Acar-Denizli, N.; Ng, W.-F.; Zeher, M.; Rasmussen, A.; Mandl, T.; Seror, R.; Li, X.; Baldini, C.; Gottenberg, J.-E.; Danda, D.; Quartuccio, L.; Priori, R.; Hernandez-Molina, G.; Armagan, B.; Kruize, A.A.; Kwok, S.-K.; Kvarnström, M.; Praprotnik, S.; Sène, D.; Bartoloni, E.; Solans, R.; Rischmueller, M.; Suzuki, Y.; Isenberg, D.A.; Valim, V.; Wiland, P.; Nordmark, G.; Fraile, G.; Bootsma, H.; Nakamura, T.; Giacomelli, R.; Devauchelle-Pensec, V.; Knopf, A.; Bombardieri, M.; Trevisani, V.-F.; Hammenfors, D.; Pasoto, S.G.; Retamozo, S.; Gheita, T.A.; Atzeni, F.; Morel, J.; Vollenveider, C.; Horvath, I.-F.; Sivils, K.L.; Olsson, P.; De Vita, S.; Sánchez-Guerrero, J.; Kilic, L.; Wahren-Herlenius, M.; Mariette, X.; Ramos-Casal 2018: How immunological profile drives clinical phenotype of primary Sjögren's syndrome at diagnosis: analysis of 10,500 patients (Sjögren Big Data Project) Clinical and Experimental Rheumatology 36 Suppl 112(3): 102-112
Delli, K.; Dagal, E.F.; Bootsma, H.; Vissink, A.; Spijkervet, F.K.L. 2018: Patient-reported change of sensibility and pain after parotid and labial gland biopsy applied for primary Sjögren's syndrome diagnostics: one-year follow-up study Clinical and Experimental Rheumatology 36 Suppl. 112(3): 173-176
Lustbader, I.; Sherman, A. 1987: Primary gastrointestinal Kaposi's sarcoma in a patient with acquired immune deficiency syndrome American Journal of Gastroenterology 82(9): 894-895
Lisker-Melman, M.; Pittaluga, S.; Pluda, J.M.; Kleiner, D.E.; Thompson, P.; Martin, P.; Yarchoan, R.; Di Bisceglie, A.M. 1989: Primary lymphoma of the liver in a patient with acquired immune deficiency syndrome and chronic hepatitis B American Journal of Gastroenterology 84(11): 1445-1448
Ruiz-Arguelles, G.J.; Ruiz-Arguelles, A.; Deleze, M.; Alarcón-Segovia, D. 1989: Acquired protein C deficiency in a patient with primary antiphospholipid syndrome. Relationship to reactivity of anticardiolipin antibody with thrombomodulin Journal of Rheumatology 16(3): 381-383
Kong, F.; Li, J-Xin.; Li, P.; Li, Y-Zhe.; Zhang, F-Chun.; Zhang, J. 2013: Association of TNFSF4 polymorphisms with susceptibility to primary Sjögren's syndrome and primary biliary cirrhosis in a Chinese Han population Clinical and Experimental Rheumatology 31(4): 546-551
Lin, Y.-K.; Yang, F.-C.; Liu, F.-C.; Lee, J.-T.; Sung, Y.-F. 2016: Co-Cccurrence of Guillain-Barre Syndrome and Primary Sjögren Syndrome in an Elderly Woman Acta Neurologica Taiwanica 25(3): 83-87
Thorel, J.B.; Deshayes, P. 1981: Digital necrosis disclosing Reynolds' syndrome (primary biliary cirrhosis and scleroderma) with Gougerot-Sjögren syndrome La Nouvelle Presse Medicale 10(27): 2295-2296
Altamar Ríos, J. 1985: Sjögren's syndrome, a manifestation of vitamin B complex deficiency. Statistical study of 98 cases in 17 years Anales Otorrinolaringologicos Ibero-Americanos 12(5): 443-457
Nelson, J.D.; Friedlaender, M.; Yeatts, R.P.; Yee, R.; McDermott, M.; Orlin, S.; Gallagher, S.C.; Shrotriya, R.C. 1998: Oral pilocarpine for symptomatic relief of keratoconjunctivitis sicca in patients with Sjögren's syndrome. the MGi PHARMA Sjögren's Syndrome Study Group Advances in Experimental Medicine and Biology 438: 979-983
Gran, J.T.; Myklebust, G. 2001: Diagnosis of primary Sjogren's syndrome Tidsskrift for den Norske Laegeforening: Tidsskrift for Praktisk Medicin Ny Raekke 121(5): 563-566
Sarkar, P.K.; Patel, N.; Furie, R.A.; Talwar, A. 2009: Pulmonary manifestations of primary Sjögren's syndrome Indian Journal of Chest Diseases and Allied Sciences 51(2): 93-101
Valtýsdóttir, S.T.; Gudbjörnsson, B.; Hällgren, R.; Hetta, J. 2000: Psychological well-being in patients with primary Sjögren's syndrome Clinical and Experimental Rheumatology 18(5): 597-600
Zambrana García, J.L.; Gallego Rojo, F.; Cruz Caparrós, G.; Díez García, F. 2001: Primary Sjogren's syndrome associated with autoimmune hepatitis Anales de Medicina Interna 18(7): 394
Pflugfelder, S.C.; Roussel, T.J.; Culbertson, W.W. 1987: Primary Sjögren's syndrome after infectious mononucleosis JAMA 257(8): 1049-1050
Wang, L.; Zhao, Y.; Zhang, F.-c. 2010: Malignant lymphoma associated with primary Sjögren's syndrome Zhonghua Yi Xue Za Zhi 90(39): 2773-2775
Sabio, J.M.; Milla, E.; Jiménez-Alonso, J. 2001: A multicase family with primary Sjögren's syndrome Journal of Rheumatology 28(8): 1932-1934