Pheochromocytoma with multiple islet cell carcinoma
Tamasawa, N.; Terada, A.; Kodama, T.; Ishigame, M.; Ishimaru, K.; Hishida, R.; Satoh, T.; Takebe, K.; Sasaki, M.; Imamura, K.
Presse Medicale 23(1): 32-34
1994
ISSN/ISBN: 0755-4982 PMID: 7907420 Document Number: 433182
We reported a rare case of a 17-year-old female with pheochromocytoma associated with multiple islet cell carcinoma. Pheochromocytoma was identified in the right adrenal gland. Multiple pancreas tumours were demonstrated unpredictably in the diagnostic imaging of the pheochromocytoma. No other endocrinological neoplasm was observed in the pituitary, thyroid and parathyroid gland. The patient underwent right adrenalectomy and total pancreatectomy. Pheochromocytoma was benign, however, pancreas tumours were non-functioning islet cell tumours and histologically malignant. This combination is assumed to represent a mixed form of multiple endocrine neoplasia (MEN) 1 and MEN 2.