Lymphangiomyomatosis: an exceptional cause of chyluria. Report of a case
Guillonneau, B.; Bouchot, O.; Buzelin, F.; Dupas, B.; Barrier, J.H.; Buzelin, J.M.
Progres en Urologie Journal de l'Association Francaise d'Urologie et de la Societe Francaise d'Urologie 3(3): 484-489
1993
ISSN/ISBN: 1166-7087 PMID: 8369828 Document Number: 412273
A rare case of lymphangiomatosis without pulmonary involvement is reported. The diagnosis was based on the presence of multifocal lesions and histological examination. Retroperitoneal lesions were responsible for chyluria, which was treated surgically. Chyluria is an exceptional complication of this disease, as only 3 such cases have been reported in the literature. The presence of cutaneous signs raises the question of the relations between lymphangiomatosis and Bourneville's tuberous sclerosis.