Dermatomyositis-like syndrome in X-linked hypogammaglobulinemia. Case-report and review of the literature
Thyss, A.; el Baze, P.; Lefebvre, J.C.; Schneider, M.; Ortonne, J.P.
Acta Dermato-Venereologica 70(4): 309-313
1990
ISSN/ISBN: 0001-5555 PMID: 1977255 Document Number: 367383
A case of dermatomyositis-like syndrome is described in a 19-year-old man with a history of Bruton's hypogammaglobulinemia. Although the patient had central-nervous-system manifestations (seizures), no echovirus was isolated in the cerebrospinal fluid, in contrast to previously reported cases. Data for our case and the 15 cases previously reported in the literature are reviewed. HLA typing of our patient revealed the presence of HLA B8 and DR3, which seems to play a major role in juvenile dermatomyositis.