Sclerosing cholangitis revealing histiocytosis X
Neveu, I.; Labrune, P.; Huguet, P.; Musset, D.; Chaussain, J.L.; Odièvre, M.
Archives Francaises de Pediatrie 47(3): 197-199
1990
ISSN/ISBN: 0003-9764 PMID: 2344248 Document Number: 354323
The case of a 3 year-old boy who presented isolated cholestasis as the initial symptom of histiocytosis X is described. Other symptoms occurred later on. Despite treatment (corticosteroid and Vinblastin), the disease continued to progress and the child died at the age of 4 1/2 years with HIV infection (contaminated blood product) and tuberculosis.