Congenital long QT syndrome in adults
Crozier, I.G.; Loughnan, A.; Dow, L.J.; Low, C.J.; Ikram, H.
New Zealand Medical Journal 102(871): 340-341
1989
ISSN/ISBN: 0028-8446 PMID: 2771275 Document Number: 329906
A family with the Romano-Ward syndrome is presented. This family showed typical features of this syndrome with QT prolongation, torsades de pointes ventricular tachycardia, sudden death and an autosomal dominant inheritance pattern. The index case presented with an exacerbation of torsades de pointes ventricular tachycardia from diuretic induced hypokalaemia, and responded to diuretic withdrawal and beta blocker therapy.