Pseudoxanthoma elasticum
Cassinelli, A.; Macedo, N.A.; Carlevaro, A.; Nicola, M.
Medicina Cutanea Ibero-Latino-Americana 14(5): 311-318
1986
ISSN/ISBN: 0210-5187 PMID: 3543550 Document Number: 281569
Four young female patients with Pseudodixanthome elasticum are reported, corresponding to the Grönblad and Strandberg syndrome. The dysplastic derangement of the elastic fibers with a potentially systemic compromise is considered, which explains the multiorganic character of the disease. We conferred to the skin changes the means of a marker that obligates an exhaustive study and follow-up of the patients to make visceral affectations.