A median craniofacial malformation: schizoprosopia. Apropos of 4 cases
Jaouen, H.; Camuzet, J.P.; Lavalou, J.F.; Le Prince, B.; Bourdinière, J.; Lallemant, J.G.; Cabanettes, J.P.
Annales d'Oto-Laryngologie et de Chirurgie Cervico Faciale Bulletin de la Societe d'Oto-Laryngologie des Hopitaux de Paris 101(4): 267-275
1984
ISSN/ISBN: 0003-438X PMID: 6465755 Document Number: 239199
Four cases of a median craniofacial malformation, schizoprosopia, are reported. This rare but compatible with life anomaly is included within the group of neurocristopathies of the nasofrontal bud. Patients affected present signs of more or less severe mediofacial division with, in some cases an associated encephalocele or cranial bone defect. The possible presence of an associated hypopituitarism must be investigated routinely, and substitutive hormone therapy combined with surgical treatment of the various malformations when results are positive.