Oculomotor signs in cerebellar disease shown in ataxia telangiectasia (Louis Bar)
Schmidt, D.
Klinische Monatsblatter für Augenheilkunde 173(3): 329-333
1978
ISSN/ISBN: 0023-2165 PMID: 108455 Document Number: 128697
Disturbances of the eye movements are described in 2 brothers with ataxia telangiectasia (Louis Bar): pathological smooth pursuit and command movements of the eyes (hypometry) with a preseved doll's phenomenon, increased reaction times of voluntary saccades, failure of gaze holding, gaze nystagmus, altered optokinetic nystagmus, and distinct convergence defect. These oculomotor defects are the result of cerebellar lesions. The E.N.G.-findings in pathologically changed pursuit movements are in accordance with those disturbances of eye movements shown by Westheimer and Blair in cerebellectomized monkeys.