Radiological aspects of diffuse pulmonary lymphangiomyomatosis
Chatel, A.; Hélénon, C.; Mudry, L.; Marsac, J.; Bigot, J.M.; Brocard, H.
Journal de Radiologie d'Electrologie et de Medecine Nucleaire 59(8-9): 455-462
1978
ISSN/ISBN: 0368-3966 PMID: 722660 Document Number: 127345
The authors report on 5 cases of diffuse pulmonary lymphangiomyomatosis. This disease occurs in women during the period of genital activity and usually presents with pulmonary signs (9/10) : dyspnoea, pneumothorax, pleural effusion, and hemoptysis. It is also found in association with renal angiomyolipomas and uterine fibromyolipomas. X-ray films of the lungs show : an interstitial syndrome, gas or fluid pleural effusions, and thoracic distention. None of these signs is constant, but the association of an interstitial syndrome with thoracic distention in a young woman appears to be specific for this affection.