Familial autoimmune hemolytic animia (AIHA) with negative Coombs test, lymphocytopenia and hypogammaglobulinemia
Roth, P.; Morell, A.; Hunziker, H.R.; Gehri, P.; Bucher, U.
Schweizerische Medizinische Wochenschrift 105(47): 1584-1585
1975
ISSN/ISBN: 0036-7672 PMID: 1209224 Document Number: 92085
A family with several cases of autoimmune hemolytic anemia and dysgammaglobulinemia is described. Two sibling had documented antierythrocyte antibodies, but a third had repeatedly negative Coombs tests. Diminished immunoglobulin-producing cells and a hypogammaglobulinemia were found, but no functional defect of humoral or cell-mediated immunity could be detected.
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