Mitral insufficiency in an incomplete form of Marfan syndrome corrected with valve replacement
Kaku, R.; Oda, T.; Fujii, Y.; Esato, K.; Yamaki, R.
Journal of Cardiovascular Surgery 16(1): 95-99
1975
ISSN/ISBN: 0021-9509 PMID: 1126990 Document Number: 89424
A 14-year-old boy with an incomplete form of the Marfan syndrome developed an acute episode of severe congestive heart failure following exertion. The preoperative studies indicated a mitral insufficiency, and a floppy, thickened mitral valve was removed and replaced with a Starr-Edwards prosthesis. Microscopically, the valve showed increase in collagen with central myxomatous transformation. Seven months postoperatively the patient is doing well and has no symptoms of heart failure.
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