Anesthesia for Charcot-Marie-Tooth Disease: Case Report
Alzaben, K.R.; Samarah, O.Q.; Obeidat, S.S.; Halhouli, O.; Al Kharabsheh, M.
Middle East Journal of Anaesthesiology 23(5): 587-590
2016
ISSN/ISBN: 0544-0440 PMID: 27487647 Document Number: 688896
Charcot-Marie-Tooth disease comprises a group of disorders characterized by progressive muscle weakness and wasting. Reviewing the anaesthetic literature produced conflicting reports about the best anaesthetic options for patients with CMTD; as they are at increased risk of prolonged response to muscle relaxants, malignant hyperthermia and risks of regional anaesthesia. We present a case of the successful use of total intravenous anaesthesia with dexmedetomidine and propofol combined with caudal block using bupivacaine mixed with dexmedetomidine without any complications, for a 17 year old male patient with Charcot Marie-Tooth disease who underwent a lower limb orthopedic surgery.