Surgical treatment of cardiovascular complications in patients with Marfan syndrome: a report of two cases and literature review
Bruls, S.; Radermecker, M.A.; Creemers, E.; Bonnet, P.; Nellessen, E.; Van Damme, H.; De Leval, L.; Defraigne, J.O.
Acta Chirurgica Belgica 112(3): 213-218
2012
ISSN/ISBN: 0001-5458 PMID: 22808762 Document Number: 659211
Cardiovascular disease is the main cause of morbidity and mortality in patients with Marfan syndrome. The most life threatening complication is aortic root aneurysms leading to aortic dissection or rupture. It can be prevented by regular aortic follow-up and prophylactic aortic surgery. Modern aortic surgery has led to a substantial increase in the life expectancy of these patients. We report two cases of Marfan syndrome with cardiovascular complications. Their management is discussed according to the most recent literature.