Rosai -Dorfman disease: a two cases report
Ben Turkia, H.; Ben Romdhane, M.; Azzouz, H.; Ben Chehida, A.; Abdelmoula, M.Slim.; Ben Abdelaziz, R.; Tebib, N.; Ben Messoud, M.; Sahtout, S.; Chelly, I.; Zitouni, M.; Mnif, E.; Ben Dridi, M.Francoise.
La Tunisie Medicale 89(5): 497-501
2011
ISSN/ISBN: 0041-4131 PMID: 21557191 Document Number: 655396
Rosai-Dorfman disease (RDD) is a benign lymphoproliferatif disorder characterized by cervical lymphadenopathies with a consistent risk of airways' compression and esthetical prejudice. Extra nodal localizations are also described. To report two pediatric cases of RDD. the first case concerned a patient with a prolonged nodal involvement of RDD. Remission seems to be natural although it coincided with a sulfaméthoxazole- triméthoprime therapy. The second case illustrated an extranodal form of RDD localized in soft tissue and paranasal sinus with extension to nasal cavity which were corticodependant. RDD is usually a benign disorder. Particular localizations, lack of effective therapy and the high risk of recurrence are important issues in this rare affection.
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