Metanephric adenofibroma: robotic partial nephrectomy of a large Wilms' tumor variant
Piotrowski, Z.; Canter, D.J.; Kutikov, A.; Al-Saleem, T.; Pei, J.; Testa, J.R.; Uzzo, R.G.
Canadian Journal of Urology 17(4): 5309-5312
2010
ISSN/ISBN: 1195-9479 PMID: 20735912 Document Number: 645362
A case of the rare, benign, Wilms' tumor (WT) variant, metanephric adenofibroma (MAF), is presented. The patient is a 21-year-old female with an incidentally discovered enhancing renal mass. The diagnosis, workup and treatment are outlined. The 19 cm renal mass was ultimately resected via robot-assisted partial nephrectomy. Pathologic diagnosis at our institution was confirmed as a MAF by the National Wilms' Tumor Study Group (NWTSG). Difficult to differentiate from WT, it is imperative that MAF be recognized and appropriately diagnosed because unlike adult WT, the natural history of MAF is indolent and adjuvant chemo/radiation therapy is rarely necessary. This case reinforces the importance of review of potential WT variants by the NWTSG.