Fatal course of a patient during in vitro fertilisation treatment

Sørensen, M.K.; Møller-Sørensen, H.; Svane, C.; Jensen, C.H.; Lange, K.H.W.; Tybjaerg-Hansen, A.

Ugeskrift for Laeger 172(20): 1537-1538

2010


ISSN/ISBN: 1603-6824
PMID: 20483102
Document Number: 640119
Chylomicronaemia syndrome is a rare disorder primarily caused by a genetic defect which increases triglycerides, combined with a secondary inducing factor. We describe the fatal course of a 33-year-old, pregnant woman with known dyslipidaemia who had been treated with in vitro fertilisation and developed chylomicronaemia syndrome with severe hypertriglyceridaemia, hypertriglyceridaemia-induced acute pancreatitis and septic shock. Appropriate treatment including close monitoring, severe restriction of dietary fat intake and early plasmapheresis is emphasized - especially during pregnancy.

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