Failure of prophylactic zinc in Wilson disease
Mishra, D.; Kalra, V.; Seth, R.
Indian Pediatrics 45(2): 151-153
2008
ISSN/ISBN: 0019-6061 PMID: 18310797 Document Number: 627730
Early institution of prophylactic therapy of asymptomatic Wilson disease patients can prevent the expression of the disease. Zinc is currently preferred therapy for presymptomatic patients. We report onset of symptomatic disease in a presymptomatic patient and deterioration of biochemical parameters in another, despite appropriate zinc therapy.
Document emailed within 1 workday
Related Documents
Yuzbasiyan-Gurkan, V.; Brewer, G.J.; Abrams, G.D.; Main, B.; Giacherio, D. 1989: Treatment of Wilson's disease with zinc. V. Changes in serum levels of lipase, amylase, and alkaline phosphatase in patients with Wilson's disease Journal of Laboratory and Clinical Medicine 114(5): 520-526Dastych, M. 1999: Serum levels of zinc, copper and selenium in patients with Wilson's disease treated with zinc Vnitrni Lekarstvi 45(4): 217-219
Lee, D.Y.; Brewer, G.J.; Wang, Y.X. 1989: Treatment of Wilson's disease with zinc. VII. Protection of the liver from copper toxicity by zinc-induced metallothionein in a rat model Journal of Laboratory and Clinical Medicine 114(6): 639-645
Mayet, I.Y. 1990: Low-dose zinc therapy for maintenance treatment of Wilson's disease Clinical Pharmacy 9(12): 951-953
Tseng, C.L.; Tsai, S.L.; Lin, K.H.; Chang, M.H.; Wang, T.R.; Hsu, Y.H.; Hsu, H.C. 1990: Wilson disease presenting as fulminant hepatic failure, acute hemolytic anemia and renal failure: report of one case Zhonghua Minguo Xiao Er Ke Yi Xue Hui Za Zhi Zhonghua Minguo Xiao Er Ke Yi Xue Hui 31(4): 266-271
Lee, H.H.; Hill, G.M.; Sikha, V.K.; Brewer, G.J.; Prasad, A.S.; Owyang, C. 1990: Pancreaticobiliary secretion of zinc and copper in normal persons and patients with Wilson's disease Journal of Laboratory and Clinical Medicine 116(3): 283-288
Nagy, J.; Vajna, M.; Dévényi, L.; Zelkó, R. 2004: Zinc sulphate release and morphology of matrices prepared for the individual therapy of Wilson's disease Die Pharmazie 59(4): 327-328
Alexiou, D.; Hatzis, T.; Koutselinis, A. 1985: Maintenance treatment of Wilson's disease with oral zinc. Apropos of a child treated for 4 years Archives Francaises de Pediatrie 42(6): 447-449
Kaur, U.; Bambery, P.; Bhushnurmath, S.R.; Deodhar, S.D.; Dilawari, J.B. 1988: Successful long term oral zinc in florid Wilson's disease: a case report Tropical and Geographical Medicine 40(2): 161-165
Herrmann, S.; Hofmann, W.; Theilmann, L. 1995: Acute liver failure as the initial manifestation of Wilson disease Medizinische Klinik 90(8): 456-461
Ghosh, L.; Shah, M.; Pate, S.; Mannari, J.; Sharma, K. 2012: Wilson's disease presenting with hypokalemia, hypoparathyroidism and renal failure Journal of the Association of Physicians of India 60: 57-59
Degli Esposti, A.; Antener, I.; Ambrosioni, G.; Bonfiglioli, G. 1976: Wilson's disease. Summary of studies carried out in a family group with Wilson's disease. Significance of amino-acid balance in homo and heterozygotes for the detection of liver damage Minerva Pediatrica 28(34): 2063-2086
Rodríguez Fariña, E.; Tremosa Llurba, G.; Xiol Quingles, X.; Lores Obradors, A.; Castellote Alonso, J.; Gornals Soler, J.B.; López Núñez, C. 2003: D-penicillamine and plasmapheresis in acute liver failure secondary to Wilson's disease Revista Espanola de Enfermedades Digestivas: Organo Oficial de la Sociedad Espanola de Patologia Digestiva 95(1): 60
Thanapirom, K.; Treeprasertsuk, S.; Komolmit, P.; Tangkijvanich, P.; Kullavanijaya, P. 2013: Comparison of long-term outcome of patients with Wilson's disease presenting with acute liver failure versus acute-on-chronic liver failure Journal of the Medical Association of Thailand 96(2): 150-156
McQuaid, A.; Lamand, M.; Mason, J. 1992: The interactions of penicillamine with copper in vivo and the effect on hepatic metallothionein levels and copper/zinc distribution: the implications for Wilson's disease and arthritis therapy Journal of Laboratory and Clinical Medicine 119(6): 744-750
Kamoun, P.; Cadoudal, M.; Rabier, D.; Jérôme, H. 1986: Detection of Wilson's disease in sibs of a patient with Wilson's disease Clinical Chemistry 32(2): 392
Kobayashi, S.; Ochiai, T.; Hori, S.; Suzuki, T.; Shimizu, T.; Gunji, Y.; Shimada, H.; Yamamoto, S.; Ogawa, A.; Kohno, Y.; Sunaga, M.; Shimazu, M.; Tanaka, K. 2001: Copper metabolism after living donor liver transplantation for hepatic failure of Wilson's disease from a gene mutated donor Hepato-Gastroenterology 48(41): 1259-1261
Malik, A.; Taneja, D.K.; Devasenapathy, N.; Rajeshwari, K. 2013: Short-course prophylactic zinc supplementation for diarrhea morbidity in infants of 6 to 11 months Pediatrics 132(1): E46-E52
Stapelbroek, J.M.; Ploos van Amstel, J.K.; van Hattum, J.; van den Berg, L.H.; Klomp, L.W.J.; Houwen, R.H.J. 2003: From gene to disease; Wilson disease: copper storage due to mutations in ATP7B Nederlands Tijdschrift Voor Geneeskunde 147(13): 603-605
Tammelleo, A.D. 1993: Failure to "fully communicate": catastrophic results. Case in point: Baptist Medical Center V. Wilson 618 So. 2d 1335--AL (1993) Regan Report on Nursing Law 34(3): 2