Langerhans cell histiocytosis located in the orbit
Lachkar, R.; Ibrahimy, W.; Benharbit, M.; Charif, C.M.; Hssissen, N.; Lezrek, M.; Karim, A.; Benchrif, Z.; Daoudi, R.
Bulletin de la Societe Belge d'Ophtalmologie 2008(309-310): 31-36
2008
ISSN/ISBN: 0081-0746 PMID: 19198550 Document Number: 621172
Langerhan's cell Histiocytosis of the orbit. Langerhan's cell Histiocytosis is a rare condition that affects children and less frequently young adults. It is characterized by a proliferation of histiocytes derived from Langerhan's cells. Orbital involvement is described in 20% of cases where orbital eosinophilic granuloma located in the frontal bone is the most frequent. The malignant nature of this disease is not established. Its evolution is unpredictable and spontaneous regression after simple biopsy were described. The authors report four cases of Langerhan's cell Histiocytosis and will discuss on the clinical and radiological aspects as well as on the evolution of orbital histiocytoses X.