Pruritic bluish-black subcutaneous papules on the chest
Laquer, V.T.; Wu, J.J.; Tournas, J.A.; Murase, J.E.; Dyson, S.W.
Dermatology Online Journal 14(3): 14
2008
ISSN/ISBN: 1087-2108 PMID: 18627715 Document Number: 618928
Steatocystoma multiplex (SM) is characterized by multiple dermal cysts involving the pilosebaceous glands. Although most presenting cases are sporadic, there is a rare familial syndrome involving a mutation in keratin 17 (K17) that is inherited in an autosomal dominant fashion. SM often presents concomitantly with eruptive vellus hair cysts (EHVS) and pachyonychia congenital type 2 (PC-2). We report a sporadic case of SM in a 21-year-old man.