Anesthetic management of a patient with hereditary fructose intolerance and phenylketonuria
Celiker, V.; Dural, O.; Erdem, K.
Turkish Journal of Pediatrics 35(2): 127-130
1993
ISSN/ISBN: 0041-4301 PMID: 8249192 Document Number: 6173
This is a report of a five-year-old girl with phenylketonuria (PKU) and hereditary fructose intolerance (HFI) who underwent elective strabismus surgery. PKU and HFI are two inborn errors of metabolism which have an autosomal recessive mode of inheritance. This case report describes the anesthetic features of a patient with PKU and HFI, each defect requiring specific anesthetic management.
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