Syringocystadenoma papilliferum: report of 8 cases
Rammeh-Rommani, S.; Fezaa, B.; Chelbi, E.; Kammoun, M.R.; Ben Jilani, S.Baltagi.; Zermani, R.
Pathologica 98(3): 178-180
2006
ISSN/ISBN: 0031-2983 PMID: 17036946 Document Number: 603777
Syringocystadenoma papilliferum (SCAP) is a rare cutaneous adnexal neoplasm with variable clinical appearance and characteristic histology. It arises in about one third of cases within a sebaceous hamartoma (SH) and in this case, multiple other benign adnexal neoplasms may be associated with it. We report the clinical and pathological data of 8 cases of syringocystadenoma papilliferum. The age at the time of the diagnosis varied from 3 to 48 years with an average age of 28 years. Three tumors were localized in the scalp, 2 in the trunk, and 3 others of unusual locations: 1 in the eyelid, 1 in the thigh and 1 in the popliteal fossa. Histopathological examination revealed 3 SCAP occurring within SH. The SCAP observed in the eyelid was associated with an apocrine cystadenoma without features of SH. The four others were not associated with any other lesion.