The use of Nd-Yag laser in the treatment of tracheal tumor in 14 years old child with mukopolisacharydosis type II
Mierzwiński, Józef.; Zwierz, A.; Jaworski, A.; Redziński, R.; Bandrowicz, Władysław.; Dalke, K.; Burduk, Pł.
Otolaryngologia Polska 60(4): 603-606
2006
ISSN/ISBN: 0030-6657 PMID: 17152817 Document Number: 601501
Hunter's Syndrome (MPS II) is a class of hereditary disorder characterized by a deficiency of specific enzyme--iduronate sulphatase required to break down mucopolisacharides and occurs in Poland in one of 100-150 thousand male live births. MPS II may be lethal in the second decade of life as a result of infiltrativ cardiomiopathy leading to irreversible heart failure or upper airway obstruction caused by infiltration, granulation and deformation in trachea or larynx. We report a case of 14-year-old male with Hunter Syndrome who developed tracheal obstruction and was treated with Nd-Yag laser. We discuss the possibility of treatment and our results--improvement in patient's symptomatic and functional status.