A case of systemic malignant atrophic papulosis (Köhlmeier-Degos' disease)
Fernández-Pérez, E.R.; Grabscheid, E.; Scheinfeld, N.S.
Journal of the National Medical Association 97(3): 421-425
2005
ISSN/ISBN: 0027-9684 PMID: 15779511 Document Number: 594616
Malignant atrophic papulosis (MAP) is a rare and clinically distinctive vasculopathy. It is characterized by narrowing and occlusion of the lumen by intimal proliferation and thrombosis, which leads to ischemia and infarction in the involved organ systems. Its rarity and rapidly fatal course make the disease a difficult diagnostic and therapeutic challenge.