Family myxoma of the heart with metachronic multiple growth
Rogov, K.A.; Sheremet'eva, G.F.; Nechaenko, M.A.
Arkhiv Patologii 66(4): 41-44
2004
ISSN/ISBN: 0004-1955 PMID: 15449689 Document Number: 568716
A case of familial heart myxoma in 4 members of one family combined with myxomic (hamartomatous) syndrome is reported. The tumor in a proband was characterized with a multiple growth in various heart chambers. Five operations were made in the proband for 16 years and seven myxomas of different locations were removed. Myxomas originating from the endocardium of the interatrial septum oval hole were removed in 3 members of his family. The case confirms the conception of heart myxoma origin from endothelial hamartia of the endocardium.