Primary neuroectodermal tumour of the kidney invading the wall of the inferior vena cava. Surgical strategy
Zini, L.; Nataf, A.; Fantoni, J.-C.; Villers, A.; Leroy, X.; Koussa, M.; Lemaitre, L.; Biserte, J.
Progres en Urologie Journal de l'Association Francaise d'Urologie et de la Societe Francaise d'Urologie 14(4): 544-547
2004
ISSN/ISBN: 1166-7087 PMID: 15776909 Document Number: 568099
Primary neuroectodermal tumours (PNET) are very aggressive malignant tumours, rapidly progressing to metastasis and death. They rarely involve the kidney, as only 23 cases have been described in the literature. Renal tumours, regardless of their histology, spread to the inferior vena cava (IVC) in 4% to 10% of cases. Invasion of the inferior vena cava wall by tumour thrombus is rare and, when it occurs, is often limited to the ostium of the renal vein. The authors report a case of primary neuroectodermal tumour of the kidney with thrombus in the inferior vena cava ascending to the right atrium (level IV), invading the wall of the IVC and associated with a non-infiltrating papillary urothelial tumour of the ureter. They describe the surgical management of this tumour and present a review of the literature.