Presentation of 2 cases of sudden deafness in patients with sickle-cell anemia and trait
García Callejo, F.J.; Sebastián Gil, E.; Morant Ventura, A.; Marco Algarra, J.
Acta Otorrinolaringologica Espanola 53(5): 371-376
2002
ISSN/ISBN: 0001-6519 PMID: 12185872 Document Number: 551179
We report two cases of sudden deafness which appeared during vaso-occlusive crisis of a sickle cell anaemia (homozygous form of disease) and a sickle cell trait (heterozygous form) in two males aged sixteen and twenty-two, respectively. A high erythrocyte aggregability and low deformability were proved in both young men. Although hearing disorders have been reported in this disease, a sudden onset is not common. The treatment used was useful in the removal of painful crisis and infections, but deafness did not improve in either of then.