Malignant histiocytofibroma of the small intestine in a young immune deficient patient
Carip, C.; de Beaumont, T.
Presse Medicale 31(5): 214-216
2002
ISSN/ISBN: 0755-4982 PMID: 11878138 Document Number: 548439
The visceral localization of malignant fibrous hystiocytoma is rare. It provokes polymorphous, rarely specific symptoms. Although muscular or cutaneous forms of the disease are frequent in the elderly, the visceral form predominates in young immunodepressed patients. An 18 year-old, HIV-seropositive man was hospitalised for chronic abdominal pain and transit disorders. Biological examination revealed eosinophilia and imaging showed a thickening of the intestinal wall of the right iliac fossa. Surgery revealed an intrinsic tumour on the intestinal wall. The anatomopathological exploration evoked a malignant storiform histiocytoma. Despite exeresis, the tumour relapsed a few months after surgery, leading to the death of the patient. This case report can be added to those of atypical localization of rare tumors in immunodepressed and young patients. The localization in the digestive tube is rare and the cases reported referred to tumors of the colon or stomach. Our case report confirms the observations of the concomitance of malignant fibrous histiocytoma and eosinophilia. The association with bacillary angiomatosic lesions is surprising and has yet to be explained.