Secreting paraganglioma of the organ of Zuckerkandl. A case report
Blin, V.; Picquet, J.; Enon, B.; Rohmer, V.
Journal des Maladies Vasculaires 27(4): 239-242
2002
ISSN/ISBN: 0398-0499 PMID: 12457132 Document Number: 541890
We report a case of a secreting retroperitoneal paraganglioma which developed on the organ of Zuckerkandl. Paraganglioma is a rare tumor of the paraganglioma system arising from undifferentiated cells of the neural crest. The originality of our observation comes from the secreting character of the tumor and the malignity proved by the local spreading to the wall of the inferior vena cava and the metastasis. The probable existence of a double primary localisation is also exceptional.