Successful operation of a symptomatic aneurysm of the superior mesenteric artery in a child with Ehlers-Danlos syndrome
Peiper, M.; Kalmár, P.; Kluth, D.; Lambrecht, W.
Der Chirurg; Zeitschrift für Alle Gebiete der Operativen Medizen 66(4): 445-447
1995
ISSN/ISBN: 0009-4722 PMID: 7634964 Document Number: 447863
Bleeding of an aneurysm - especially of a great vessel - represents a complication of Ehlers-Danlos syndrome that is often lethal. A successful operation of a symptomatic aneurysm of the superior mesenteric artery in a 12-year old girl with an Ehlers-Danlos syndrome type VI is reported. The aneurysm was resected and replaced by a venous graft. Four years postoperatively the artery is perfectly patent; a new aneurysm did not develop.