Multiple paraganglioma
Llobell Segui, G.; Martínez Ruiz, M.; Peralba Vaño, J.I.; Toral Revuelta, J.R.; Martos Peregrín, J.A.
Anales de Medicina Interna 10(11): 553-555
1993
ISSN/ISBN: 0212-7199 PMID: 8117872 Document Number: 421771
Paragangliomas are tumors of the chromaffin system producing catecholamines and both the adrenal extra-adrenal type have a common origin at the neural crest, which has been supported by the similarities of the paraganglions both from a histological and functional perspective. Most of the extra-adrenal paragangliomas are bending and non-functional. In addition, they are usually confined to just one site. We present the case of a young patient with benign multiple paraglanglioma in two different locations, juxtahepatic and juxtacarotic (Chemodectoma) and, thus, far away from each other. The extra-abdominal location is very rare, with a frequency lower than 2%. In addition, one of paraganglions was functional and the other one was not. Initially, a surgical intervention was performed on the functional abdominal tumoration and latter, another intervention was performed at the cervical level, both with excellent results. We also highlight the good response to the postoperative therapy with Prazosin.