Familial cherubism (report of 10 cases)
Wu, Y.T.
Zhonghua Kou Qiang Yi Xue Za Zhi 28(3): 148-50 190-1
1993
ISSN/ISBN: 1002-0098 PMID: 8275805 Document Number: 416325
10 cases of familial cherubism were presented. Of them, there were 7 patients under 9 years of age. Painless swelling of the mandible was exclusively complained. The lesions often occurred bilaterally (9/10), resulting in "square jaw" deformity. The radiographs usually revealed multicystic appearance with various opacities (8/10) and widen, sclerotic margins (7/10). Other common manifestations included impaction and absence of teeth (7 for each) and twisted roots (6/10). At follow up for 3 years and 5 months, the lesions in 2 cases without operation tended to be steady or unchanged radiographically. In 3 cases treated by enucleation, no recurrence was noted at follow-up for 1 year and 2 months, 10 years and 9 months, and 15 years and 4 months after operation respectively.