Correction of transposition of great vessels with and without associated congenital defects. Description of two clinical cases
Pellicelli, A.M.; Barba, J.; Huelmos, A.; Cipriani, G.; Borgia, M.C.
Minerva Cardioangiologica 41(4): 153-156
1993
ISSN/ISBN: 0026-4725 PMID: 8332272 Document Number: 411444
We describe two cases of corrected transposition of great vessel (L Transposition). The first case was diagnosed in a man of 70 years old and was not associated with other congenital defects. The second case regards a young man of 16 years old and congenital cardiopathy was associated with interventricular defect and left Ebstein disease. We discuss the different evolution of L Transposition according to the presence or not of other congenital defects and we analyse right ventricle behaviour when it is submitted systemic pressure. In the literature only 26 cases of L Transposition were described in patients over 40 years old. The first case represents a rarity and it shows how in the absence of associated congenital defects, the right ventricle is able to adapt to systemic pressure. Bidimensional echocardiography in the method of choice to diagnose and evaluate congenital cardiopathy in adult age.