Lymphangioleiomyomatosis with chylous ascites
Raymond, A.A.; Isa, M.R.; Abdullah, T.; Kudva, M.V.
Singapore Medical Journal 34(3): 276-278
1993
ISSN/ISBN: 0037-5675 PMID: 8266193 Document Number: 410388
A 41-year-old Malay housewife presented with recurrent chylous ascites and progressive cachexia over 17 years. A diagnosis of lymphangioleiomyomatosis (LAM) was established by laparotomy where biopsy of the liver, peritoneum and adhesions from previous surgery showed smooth muscle proliferation in the blood vessels and lymphatics. Clinically and radiologically, there was no evidence of pulmonary involvement. She was treated with dietary fat restriction and medium-chain triglycerides. This is the first case of LAM reported in Malaysia.