Functional pulmonary atresia: a case report
Umebayashi, Y.; Arikawa, K.; Chosa, N.; Kinjo, T.; Nishida, S.; Tabata, D.; Haraguchi, T.; Aihoshi, S.; Seki, S.; Umemoto, K.
Kyobu Geka. Japanese Journal of Thoracic Surgery 45(7): 644-646
1992
ISSN/ISBN: 0021-5252 PMID: 1619832 Document Number: 397065
A male neonate, two days of age, was admitted with cyanosis and tachypnea. Chest roentgenograms showed massive cardiomegaly and decreased pulmonary vasculatures. Echocardiographic and the right ventriculographic findings were interpreted as showing primary pulmonary atresia with secondary tricuspid incompetence. At a Brock operation, however, there was no resistance in passing the instrument through the pulmonary valve. The baby died twelve hours after surgery. Postmortem examination showed that the tricuspid regurgitation was a cause of the functional pulmonary atresia (FPA). It is important to distinguish FPA from pure pulmonary atresia because conservative therapy is the first choice for the FPA.