Drash syndrome
Coze, C.; Gentet, J.C.; Chapuis, E.; Picon, G.; Guys, J.M.; Panuel, M.; Scheiner, C.; Raybaud, C.
Pediatrie 47(11): 757-760
1992
ISSN/ISBN: 0031-4021 PMID: 1342416 Document Number: 396852
The authors report one case of Drash syndrome: association of Wilms' tumor, nephropathy and genital abnormalities. The definition, prognosis and origin of this triad are discussed.
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