Pachyonychia congenita tarda. a late-onset form of pachyonychia congenita
Paller, A.S.; Moore, J.A.; Scher, R.
Archives of Dermatology 127(5): 701-703
1991
ISSN/ISBN: 0003-987X PMID: 1827243 Document Number: 381694
Pachyonychia congenita is an autosomal dominant disorder that usually develops in early infancy. We have observed five patients with the onset of the typical subungual hyperkeratoses of pachyonychia during the teenage years. Leukokeratosis and keratoderma of the palms and soles were associated. The family history of three of the patients suggests that pachyonychia congenita tarda is also inherited in an autosomal dominant manner.