Atresia of the pulmonary artery with intact intraventricular septum
Berishvili, I.I.; Nasedkina, M.A.; Vaulina, T.N.; Ungiadze, M.N.
Arkhiv Patologii 50(6): 41-48
1988
ISSN/ISBN: 0004-1955 PMID: 3178514 Document Number: 315232
Cardiological studies of 16 patients with atresia of the pulmonary artery (APA) and intact interventricular septum (IIS) provided evidence for the following inferences: 1) most hearts in this pathology are characterized by right ventricular (RV) hypoplasia which determines structural defects of the ventricle dependent in their severity on restriction capacity of the right atrioventricular valve and time from the onset of reduced RV blood flow 2) common anatomical features of the defect are complete RV obstruction due to valvular atresia, IIS and normal shape of the conus, RV myocardial hypertrophy 3) survival of the patients conditioned by interatrial communication and open arterial canal. According to the authors, there are three types of APA with IIS. Type I--normal right ventricle with distinct components: sinuous, conical, trabecular. Type II--hypoplastic right ventricle with blocked function of the trabecular component. Type III--right ventricle affected by advanced hypoplasia and with operable sinuous part only.