Epilepsy with bilateral occipital calcifications: a benign onset with progressive severity
Gobbi, G.; Sorrenti, G.; Santucci, M.; Rossi, P.G.; Ambrosetto, P.; Michelucci, R.; Tassinari, C.A.
Neurology 38(6): 913-920
1988
ISSN/ISBN: 0028-3878 PMID: 3368073 Document Number: 311927
We studied four patients with a focal epilepsy and bilateral occipital corticosubcortial calcifications without any sign of phakomatosis. The clinical course of the disease was similar in all the patients and evolved from a benign onset to a severe encephalopathy with progressive mental impairment. The question of whether these patients have an incomplete and a typical form of Sturge-Weber syndrome or a previously undescribed disorder is addressed.