Pulmonary arterial hypertension as a manifestation of lupus erythematosus
Stark, P.; Sargent, E.N.; Boylen, T.; Jaramillo, D.
Der Radiologe 27(8): 370-374
1987
ISSN/ISBN: 0033-832X PMID: 3659344 Document Number: 298243
We present five patients with systemic lupus erythematosus (SLE) who developed pulmonary arterial hypertension and cor pulmonale in the course of their disease. The clinical features, as well as, the radiological manifestations of this rare manifestation of SLE are discussed. A vasculitic process is the most likely cause of this complication. Therapy is ineffective and the prognosis is poor.