Vascular complications in the Ehlers-Danlos syndrome
Krog, M.; Almgren, B.; Eriksson, I.; Nordström, S.
Acta Chirurgica Scandinavica 149(3): 279-282
1983
ISSN/ISBN: 0001-5482 PMID: 6613464 Document Number: 218325
The Ehlers-Danlos syndrome is a rare condition, which usually is easily recognized. In one type of this disease, type IV, arterial fragility dominates, and the syndrome may remain undiscovered until the patient has a traumatic or spontaneous arterial rupture. Two cases with a fatal outcome are presented in order to emphasize some important aspects in the management of these patients.