An extreme case of Lobstein's osteopsathyrosis: problems of surgical correction
Huscher, C.; Conti, L.; Vianini, S.; Taglietti, G.; Huscher, M.
La Pediatria Medica e Chirurgica Medical and Surgical Pediatrics 4(5): 565-569
1982
ISSN/ISBN: 0391-5387 PMID: 6927360 Document Number: 194497
Those surgeons who have had experience of Sofield's treatment in case of osteogenesis inperfecta would be unanimous in agreeing that this method offers great advantages to these unfortunate children. Although the technic is exact and the results often cancelled out by the growth so that the re-operation is indicated, nevertheless the long fracture-free period gained and the control of deformity confer very worth-while benefits. A case of O.I. is reported; the subject presented fracture sequaele in the lower limbs and bone alterations of extreme seriousness. Sofield's treatment was not possible in the rodding time; the Authors describe a modified treatment which has proved useful in practice. Notes on the specific features, course and treatment are presented; a particular attention is paid to its genetic and etiopathogenetic aspects.