Familial Hibernian fever
Williamson, L.M.; Hull, D.; Mehta, R.; Reeves, W.G.; Robinson, B.H.; Toghill, P.J.
Quarterly Journal of Medicine 51(204): 469-480
1982
ISSN/ISBN: 0033-5622 PMID: 7156325 Document Number: 184843
An Irish family with an unusual periodic syndrome is described. Attacks consist of fever with localized myalgia and painful erythema. Other features include abdominal pain and pleurisy, with leucocytosis and a high ESR. The syndrome resembles classical familial Mediterranean fever (FMF) but differs from it in its prompt response to steroids and its autosomal dominant pattern of inheritance. The disease appears to have a benign course and no patient has developed amyloid.