Hemolytic anemia after open heart surgery of endocardial cushion defect with polysplenia syndrome
Saga, T.; Iemura, J.; Kusumoto, Y.; Wakaki, N.; Katayama, O.; Oka, H.; Noritake, S.; Nishioka, T.; Oku, H.; Kawai, J.; Sunagawa, A.; Nakamura, Y.; Shinohara, T.; Yokoyama, T.; Shirotami, H.
Nihon Geka Hokan. Archiv für Japanische Chirurgie 50(6): 904-910
1981
ISSN/ISBN: 0003-9152 PMID: 7337514 Document Number: 169555
A 2 yr old female who had severe hemolytic anemia after open heart surgery of endocardial cushion defect (ECD) was presented. She had undergone incomplete repair of ECD (the 1st time) in another hospital. The mitral annuloplasty, the repair of the mitral cleft and closure of the ostium primum defect were carried out at the 2nd operation. The etiology of the hemolysis was considered due to a jet stream of regurgitant blood through the remnant cleft of the mitral valve against a rough surface of the autopericardial patch which was used to close the defect at the 2nd operation. To prevent the hemolysis, a smooth surface prosthesis, such as Gore-Tex sheet or fresh autopericardial patch, should be used to close the atrial septal defect because complete repair of the mitral regurgitation is occasionally difficult in complete atrioventricular canal or in the patients with mitral cleft.